ICNC Abstracts, ICNC 2018

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Hemiconvulsion Hemiplegia Epilepsy Syndrome: A case Report
DEEPAK DWIVEDI, Chitra soni, jyoti singh

Last modified: 2018-09-09

Abstract


Introduction: Hemiconvulsion hemiplegia epilepsy (HHE) syndrome is a rare complication of prolonged focal seizures in children upto 4 years of age. It is idiopathic and seen in the setting of febrile seizures in otherwise normal children but less commonly is also associated with structural, infective, traumatic and degenerative diseases that predispose to seizures. It has 3 stages, the first of prolonged focal seizures, then  hemiplegia and followed by final stage of development of epilepsy after a variable latent period. Case Report:  A 5month old girl former full term infant delivered vaginally presented with history of fever followed by seizure and unilateral weakness of body. There was no prior history of seizure and her motor and language development was age appropriate. Her parents stated that she was in her usual state of health and was acting normally, and then she developed fever. She developed seizure after few hour of fever for which patient came to hospital with active seizure for which she receive i/v  midazolam, phenytoin , valproate and levtiracetam. Following seizure patient developed weakness of left side of body. The total duration of seizure approximately was 10-15 hours. MRI scans showed diffuse right hemicerebral diffusion restriction while left cerebral cortex was normal. As of last followup at 6 months of age baby didn’t had seizures and was on maintainence dose of syrup levtiracitam. HHE is a potentially reversible complication of prolonged focal seizures, so prolonged focal seizures should be managed urgently and appropriately to prevent long term sequelae.

 

 


Keywords


hemoconvulsion, hemiplegia, epilepsy

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